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Multiple Symmetric Lipomatosis (Madelung’s disease): Clinical Observations

Abstract

Multiple symmetric lipomatosis also known as Madelung's disease is a rare disease of unknown etiology, characterized by a marked increase in non-encapsulated fatty mass in the first place around the neck, upper body and back. Currently, there is only about 300 cases with this pathology. The reason for the emergence and development of multiple symmetric lipomatosis is alcohol, which can act as a cofactor in the development of lipomatosis. Diagnosis is based on history, physical examination of the patient. Choices in diagnostic activities is computed tomography which allows preoperative determine the spread and invasion of fat mass in the surrounding soft tissue.

About the Author

Anton Vsevolodovich Malyshev
A.V. Vishnevsky Institute of Surgery
Russian Federation


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Review

For citations:


Malyshev A.V. Multiple Symmetric Lipomatosis (Madelung’s disease): Clinical Observations. Medical Visualization. 2014;(3):59-68. (In Russ.)

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ISSN 1607-0763 (Print)
ISSN 2408-9516 (Online)