CT Scan of the Temporal Bone in the Diagnosis of Congenital CSF-Fistula or Perilymphatic Gusher Syndrome. Clinical Case Observation

We present a rare case of congenital malformations of the internal auditory canal with the presence CSF- perilymphatic fistula. The fistula occurring clinically under the mask of otosclerosis. However, traditionally used in otosclerosis surgery on the stapes in this case will inevitably lead to a sudden expiration of CSF from the window of the vestibule. Such intraoperative complication is called perilymphatic gusher (fountain) syndrome. Patients with congenital perilymphatic fistula surgery on the stapes contraindicated because it not only solves the problem of hearing impairment, but can lead to meningitis, deafness, and severe dizziness in the postsurgery period. The only method that before surgery allows to reliably distinguish between otosclerosis and congenital malformation of the internal auditory canal with CSF-perilymphatic fistula, is computed tomography. The article shows possibilities of a CT of the temporal bone and the efficiency of use of GE Healthcare CT with unique spatial resolution of GSI detectors in the preoperative diagnosis and prevent severe complications.

компьютерная томография височных костей, ликворно-перилимфатическая фистула, gusher-синдром, отосклероз, внутренний слуховой проход, анкилоз стремени, computed tomography of the temporal bone, cerebrospinal-perilymphatic fistula, gusher syndrome, otosclerosis, internal auditory canal, stapes ankylosis

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