Monolobar Form of Caroli’s Disease with Intrahepatic Stone (Clinical Case)
https://doi.org/10.24835/1607-0763-2017-2-85-89
Abstract
Caroli’s disease is a rare inherited disorder characterized by nonobstructive saccular or fusiform dilation of the intrahepatic bile ducts. Two main types of Caroli’s disease are reported, the true type with isolated dilation of intrahepatic bile ducts of single liver segment with formation of stones and development of cholangitis. The second type is combined with a congenital hepatic fibrosis. The true type of Caroli’s disease is distinct from primary sclerosing cholangitis, polycystic disease, cholangiolithiasis and other diseases. This paper presents a literature review and a case of monolobar Caroli’s disease with intrahepatic stones. The difficulties of preoperative differential diagnosis are shown.
About the Authors
T. N. Galyan
B.V. Petrovsky National Research Centre of Surgery
Russian Federation
Russian Federation
Tatiana N. Galyan – cand. of med. sci., the senior research of XRay and CT diagnostic department
Contact: Abrikosovsky 2, Moscow, Russia, 119991.
N. S. Tarba
B.V. Petrovsky National Research Centre of Surgery
Russian Federation
Competing Interests: Naala S. Tarba – graduate student of XRay and CT diagnostic department
Russian Federation
Competing Interests: Naala S. Tarba – graduate student of XRay and CT diagnostic department
V. V. Khovrin
B.V. Petrovsky National Research Centre of Surgery
Russian Federation
Valery V. Khovrin – doct. of med. sci., head of XRay and CT diagnostic department
Russian Federation
Valery V. Khovrin – doct. of med. sci., head of XRay and CT diagnostic department
L. O. Polizhuk
B.V. Petrovsky National Research Centre of Surgery
Russian Federation
Lilya O. Polizhuk – cand. of med. sci., doctor of coloproctology department
Russian Federation
Lilya O. Polizhuk – cand. of med. sci., doctor of coloproctology department
N. N. Bagmet
B.V. Petrovsky National Research Centre of Surgery
Russian Federation
Nikolay N. Bagmet – doct. of med. sci., the leading research of liver surgery
Russian Federation
Nikolay N. Bagmet – doct. of med. sci., the leading research of liver surgery
E. P. Fisenko
B.V. Petrovsky National Research Centre of Surgery
Russian Federation
Elena P. Fisenko – doct. of med. sci., the main research of ultrasound department
Russian Federation
Elena P. Fisenko – doct. of med. sci., the main research of ultrasound department
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Review
For citations:
Galyan T.N., Tarba N.S., Khovrin V.V., Polizhuk L.O., Bagmet N.N., Fisenko E.P. Monolobar Form of Caroli’s Disease with Intrahepatic Stone (Clinical Case). Medical Visualization. 2017;(2):85-89. (In Russ.) https://doi.org/10.24835/1607-0763-2017-2-85-89
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